Case 6 / 2014 - Five-year Old Child with Scimitar Syndrome and Pulmonary Sequestration of Right Lower Lobe
نویسنده
چکیده
Bi-Doppler echocardiogram: showed a clear enlargement of right cavities, dilation of the pulmonary trunk and left pulmonary artery. 5 mm ostium secundum interatrial communication with shunt from the left to the right. Pulmonary veins on the left normally drain in normal left atrium and right veins on the dilated inferior vena cava, next to the right atrium. Measurements: RV = 26, LV = 31, PT = 21, RPA = 7, LPA = 13, annulus T = 22, annulus M = 16, annulus P = 15 annulus Ao = 15 mm, RVSP = 37 mmHg, LVEF = 66%, (Figure 2). Cardiac catheterization confirmed the diagnosis of Scimitar syndrome with abnormal draining of right pulmonary veins in inferior vena cava and interatrial communication. It was verified with an injection of contrast agent in the descending aorta the presence of systemic-to-pulmonary collateral vessel which was being directed to the right lower lobe (pulmonary sequestration) and underwent embolization by placing four spring coils (Figure 2). Pressures: RA = 11, RV = 40/12, PT = 36/8-17, PC = 16, LA = 12, LV = 82/17, Ao = 90/60-70 mmHg.
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